@misc{schmutzhard_pelizaeus_merzbacher_2009, author={Schmutzhard, J.,Schwentner, I.,Glueckert, R.,Sergi, C.,Beckmann, F.,Abraham, I.,Riechelmann, H.,Schrott-Fischer, A.,Mueller, B.}, title={Pelizaeus Merzbacher disease: morphological analysis of the vestibulo-cochlear system}, year={2009}, howpublished = {journal article}, doi = {https://doi.org/10.1080/00016480802698866}, abstract = {In agreement with previously published findings, our results demonstrate that Pelizaeus Merzbacher disease (PMD) does not affect the development and morphology of the peripheral vestibulo-cochlear system. Objective: PMD is a consequence of X-linked mutation of the main central nervous system (CNS) myelin protein resulting in a complex neurological syndrome. Otorhinolaryngological symptoms include nystagmus and alterations of auditory-evoked brainstem responses. To date no histopathological analysis of the inner ear has been performed. Materials and methods: The temporal bone morphology of an affected fetus was examined with light microscopy and synchrotron radiation-based micro computed tomography. Results: The regular structure of the vestibulo-cochlear system was shown in this multi-modular analysis.}, note = {Online available at: \url{https://doi.org/10.1080/00016480802698866} (DOI). Schmutzhard, J.; Schwentner, I.; Glueckert, R.; Sergi, C.; Beckmann, F.; Abraham, I.; Riechelmann, H.; Schrott-Fischer, A.; Mueller, B.: Pelizaeus Merzbacher disease: morphological analysis of the vestibulo-cochlear system. Acta Oto-Laryngologica. 2009. vol. 129, no. 12, 1395-1399. DOI: 10.1080/00016480802698866}}